Linfangiectasia intestinal primaria: primer reporte de caso en Perú

Katherine M. Usnayo Usnayo, Alejandro Piscoya, Raffo Escalante Kanashiro, Suly Sánchez Dávila

Resultado de la investigación: Contribución a una revistaArtículoInvestigaciónrevisión exhaustiva

Resumen

Primary intestinal lymphangiectasia is a rare clinical condition of unknown etiology. The common age of presentation is during the first 3 years of life, but cases in adults have also been reported. It has a variable symptomatology, but the main clinical manifestation is edema, also diarrhea and weight loss can occur. The loss of lymph fluid into the gastrointestinal tract also leads to hypoproteinemia and lymphopenia. Diagnosis is based on clinical manifestations, laboratory and endoscopic findings, and is confirmed on histopathological examination of biopsy. The main treatment is a protein rich, low in fat and medium chain triglyceride diet. We present the case of a 1-year-old male patient who presents with generalized edema, predominantly in lower limbs, and diarrhea. Laboratory findings show the presence of marked hypoproteinemia. Then an endoscopy and a duodenal biopsy are performed, and the histopathological study confirms the diagnosis of primary intestinal lymphangiectasia. The patient is treated and after a satisfactory evolution, is discharged.
Idioma originalEspañol
Páginas (desde-hasta)78-80
Número de páginas3
PublicaciónRevista de gastroenterologia del Peru : organo oficial de la Sociedad de Gastroenterologia del Peru
Volumen39
N.º1
EstadoPublicada - 1 ene 2019

Huella dactilar

Intestinal Lymphangiectasis
Hypoproteinemia
Peru
Biopsy
Diarrhea
Edema
Clinical laboratories
Lymphopenia
Endoscopy
Lymph
Nutrition
Oils and fats
Gastrointestinal Tract
Weight Loss
Lower Extremity
Triglycerides
Fats
Diet
Proteins
Fluids

Citar esto

Usnayo Usnayo, Katherine M. ; Piscoya, Alejandro ; Escalante Kanashiro, Raffo ; Sánchez Dávila, Suly. / Linfangiectasia intestinal primaria : primer reporte de caso en Perú. En: Revista de gastroenterologia del Peru : organo oficial de la Sociedad de Gastroenterologia del Peru. 2019 ; Vol. 39, N.º 1. pp. 78-80.
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Linfangiectasia intestinal primaria : primer reporte de caso en Perú. / Usnayo Usnayo, Katherine M.; Piscoya, Alejandro; Escalante Kanashiro, Raffo; Sánchez Dávila, Suly.

En: Revista de gastroenterologia del Peru : organo oficial de la Sociedad de Gastroenterologia del Peru, Vol. 39, N.º 1, 01.01.2019, p. 78-80.

Resultado de la investigación: Contribución a una revistaArtículoInvestigaciónrevisión exhaustiva

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